National Academy of Agricultural Sciences (NAAS)
|
PRINT ISSN : 2319-7692
Online ISSN : 2319-7706 Issues : 12 per year Publisher : Excellent Publishers Email : editorijcmas@gmail.com / submit@ijcmas.com Editor-in-chief: Dr.M.Prakash Index Copernicus ICV 2018: 95.39 NAAS RATING 2020: 5.38 |
Lymphangioleiomyomatosis (LAM) is a rare disorder resulting from proliferation in the lung, kidney, and axial lymphatics of abnormal smooth muscle–like cells (LAM cells) that exhibit features of neoplasia and neural crest origin. Cystic destruction of the lung with progressive pulmonary dysfunction and the presence of abdominal tumors.LAM can occur with increased frequency in patients with tuberous sclerosis complex (TSC), an autosomal dominant disorder due, in part, to mutations in the TSC1 or TSC2 gene. Here in the study present a 55 year old female with shortness of breath and reduced exercise capacity after complete investigation diagnosed as Lymphangioleiomyomatosis.Though there is availability of excellent imaging methods, histological examination are the gold standard tools for the final diagnosis.
Citations |
 |
 |
 |
 |
